Skip to main content

Table 5 The clinical therapeutic and outcome of 50 AIE children

From: Clinical characteristics and management of autoimmune enteropathy in children: case reports and literature review

Clinical therapeutic

N = 50

Outcome

Simple glucocorticoids

7(14%)

Clinical remission

Immune drugs

31(62%)

26 cases clinical remission(83%)

Tacrolimus

18

4 cases died, 14 cases Clinical remission(77%)

Azathioprine

9

1 case died, 8 cases Clinical remission(88%)

Cyclosporine

2

Clinical remission

Cyclophosphamide

2

Clinical remission

Parenteral nutrition

4(8%)

Partial remission of Intestinal symptoms, but no remission of growth retardation