Fig. 3

Case 1. Computed tomography (CT) and endoscopic retrograde cholangiopancreatography (ERCP) images of a 3.1-year-old patient are shown in (a) and (b). Pancreatic stones were found in the pancreatic head, and the pancreatic duct was dilated. CT and ERCP images at 6.3 years of age are shown in (c) and (d). Atrophy of the tail of the pancreas and decreased exocrine function were also observed. Several ERCP attempts were in vain; thereafter, Longitudinal pancreaticojejunostomy with coring-out of the pancreatic head (Frey’s procedure) was performed at 7-years of age, and there has been no occurrence of pancreatitis since. Arrowhead: pancreatic head, pancreatic duct; Arrow: pancreatic tail