Characteristics | NC/C < 2 | NC/C > 2 | p-value |
---|---|---|---|
n = 23 | n = 24 | ||
Age of diagnosis (months) | 7.2 (2.2–34) | 6.8 (3.5–44.5) | 0.52 |
0–1(Y) | 13 (56.5%) | 15 (62.5%) | – |
1–15 (Y) | 10 (43.5%) | 9 (37.5%) | 0.68 |
Sex ratio (female: male) | 48:52 (11:12) | 50:50 (12:12) | 0.88 |
Weight – median (IQR), kg | 6.5 (5.5–12.3) | 7.5 (5.4–11.3) | 0.57 |
NYHA class/ Ross at diagnosis – n (%) | |||
I | 5 (21.7%) | 4 (16.7%) | – |
II | 9 (39.1%) | 3 (12.55) | – |
III | 6 (26.1%) | 7 (29.2%) | – |
IV | 3 (13%) | 10 (41.7%) | 0.03 |
Arrhythmia/abnormal findings on electrocardiography | 9 (39.1%) | 18 (75%) | 0.01 |
Thromboembolic | 0 (0%) | 1 (4.2%) | 0.32 |
Family history | 1 (4.3%) | 1 (4.2%) | 0.97 |
LVEF-median (IQR) | 46.5 (36.3–51) | 35 (31–44.5) | 0.07 |
FS-median (IQR) | 22.5 (17.5–26) | 16 (14.5–22) | 0.07 |
NC/C ratio: median (IQR) | 1.5 (1.4–1.8) | 2.4 (2.2–3.1) | < 0.01 |
Number of deaths | 3 | 12a | 0.01 |
Median (IQR) duration of follow-up, months | 12 (6–24) | 10 (1–42.3) | 0.69 |