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Table 1 Characteristics of patients reported as number and percentage or mean ± SD

From: Exacerbations and Pseudomonas aeruginosa colonization are associated with altered lung structure and function in primary ciliary dyskinesia

 ChildrenAdults
Number of patients(%)21(36.2)37(63.8)
PCD positive18(85.7)33(89.2)
PCD highly likely3(14.3)4(10.8)
Males(%)7(33.3)19(51.3)
Age in years(mean ± SD)11.1 ± 4.639.4 ± 14.4
Age at diagnosis(mean ± SD)4.3 ± 4.226.5 ± 16.2
Situs inversus(%)14(66.6)22(59.4)
Situs solitus(%)6(28.6)15(40.5)
Situs ambiguous(%)1(4.8)0(0.0)
Lobectomy(%)1(4.8)5(13.5)
Percentage of predicted value
FEV1(mean ± SD)93.3 ± 18.772.5 ± 23.4
FVC(mean ± SD)103.5 ± 15.685.2 ± 21.7
Exacerbations(mean ± SD)1.6 ± 1.02.3 ± 1.1
Exacerbations ≥ 2/year(%)10(47.6)26(70.3)
Colonization by:
Pseudomonas aeruginosa3(14.3)12(32.4)
Other pathogens9(42.8)9(24.3)
Chest CT score (mBhalla)2.6 ± 6.216.2 ± 9.5
Bronchiectasis(%)6(28.6)32(86.5)
Lobes(mean ± SD)0.6 ± 12.5 ± 1.3
Severity of bronchiectasis
BSI2.5 ± 3.15.1 ± 4.3
FACED0.4 ± 0.81.2 ± 1.2
eFACED0.8 ± 1.42.1 ± 2.0