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Table 2 Comparison of CPT1A P479L homozygosity in unexpected infant death cases (SIDS, SUDI and infection) occurring in Nunavut (July 1, 1999-June 30, 2011) to the estimated population P479L homozygosity [24], by region and territory

From: Causes and risk factors for infant mortality in Nunavut, Canada 1999–2011

 

Cases

Population

Odds Ratio

(95%CI)

2 sided FET p

 

n

f

(95%CI)

n

f

(95%CI)

   

NUNAVUT

30

85.7

(69.7-95.2)

442

63.6

(59.9-67.2)*

3.43

(1.30-11.47)

0.006

 Qikiqtani

8

88.9

(51.8-99.7)

162

53.6

(47.8-59.4)*

6.91

(0.90- 308.87)

0.044

 Kivalliq

16

88.9

(62.5-98.6)

170

70.0

(63.8-75.7)

3.44

(0.77-31.45)

0.108

 Kitikmeot

6

75.0

(34.9-96.8)

110

73.3

(65.5-80.2)

1.09

(0.19-11.47)

1.000

 Kivalliq & Kitikmeot (combined)

22

84.6

(65.1-95.6)

290

71.2

(66.5-75.7)

2.22

(0.73-9.04)

0.178

  1. * Genotype frequencies deviated from Hardy-Weinberg equilibrium (p<0.05) [24].
  2. f = frequency. CI = confidence interval. FET = fisher’s exact test.