From: Clinical and mutational features of Vietnamese children with X-linked agammaglobulinemia
Patient | 1 | 2 | 3 | 4 | Reference values | |
---|---|---|---|---|---|---|
WBC (×109/L) | 15.1 | 9.4 | 8.8 | 4.6 | 5-10 | |
Neutrophils (×109/L) | 11.2 | 5.1 | 4.3 | 2.1 | 1.5-5 | |
Lymphocytes (×109/L) | 3.7 | 4,2 | 4.4 | 2.4 | 1.5-5 | |
Ig (g/l) | IgG | 0.06 | 2.18 | 1.7 | 0.01 | 6-15 |
IgA | < 0.01 | 0.03 | 0.02 | 0.01 | 1.5-2.25 | |
IgM | < 0.01 | 0.21 | 0.06 | 0.13 | 0.75-1.5 | |
CD19+ (%) (/μL) | < 0.1 | < 0.1 | < 0.1 | 1.9 (58) | 6-25 | |
CD3+ (%) (/μL) | 95 (3535) | 93 (3564) | 89 (3982) | 95 (2335) | 55-84 | |
CD4+ (%) (/μL) | 29 (1078) | 45 (1707) | 36 (1616) | 15 (367) | 31-60 | |
CD8+ (%) (/μL) | 59 (2209) | 37 (1404) | 47 (2102) | 73 (1792) | 13-41 | |
CD4+/CD8+ | 0.49 | 1.22 | 0.77 | 0.2 | 0.9-3.1 |