From: Neonatal Hyperbilirubinemia in infants with G6PD c.563C > T Variant
Variables | G6PD normal | G6PD deficient | G6PD Variants | Â | P-value | |
---|---|---|---|---|---|---|
 |  |  | c.563C > T | c.131C > G | Unknown |  |
n | 184 | 32 | 21 | 3 | 8 | Â |
Weight (kg) | 2.7 ± 0.7 | 2.9 ± 0.6 | 2.9 ± 0.5 | 2.6 ± 0.8 | 2.8 ± 1.0 | 0.157 |
Age at presentation (days) | 2.2 ± 2.2 | 1.6 ± 1.3* | 1.6 ± 1.4 | 1.6 ± 0.6 | 1.5 ± 1.1 | 0.215 |
Icterus in first 24 h of life n (%) | 63(33.7) | 15(46.9) | 10(47.6) | 1(33) | 4(50) | <0.001** |
Hemoglobin (g/dl) | 16.5 ± 2.5 | 15.5 ± 1.9* | 15.7 ± 2.09 | 13.9 ± 0.32 | 15.7 ± 1.8 | 0.172 |
Retic count (%) | 4.0 ± 2.2 | 5.0 ± 2.5* | 4.9 ± 2.5 | 5.1 ± 0.8 | 5.0 ± 3.2 | 0.140 |
G6PD activity (U/gHb) | 14.0 ± 4.5 | 0.6 ± 0.9* | 0.3 ± 0.2 | 2.2 ± 2.2 | 1.6 ± 2.3 | <0.001** |
TSH (μIU/ml) | 5.9 ± 4.7 | 6.9 ± 4.5 | 7.0 ± 4.3 | 12.2 ± 9.2 | 5.1 ± 3.2 | 0.355 |
Peak bilirubin (mg/dl) | 13.8 ± 4.6 | 16.7 ± 6.0* | 16.8 ± 5.4 | 14.9 ± 1.2 | 17.2 ± 8.8 | 0.008** |
Age at peak bilirubin (days) | 4.3 ± 2.3 | 2.6 ± 1.9* | 2.9 ± 1.6 | 1.6 ± 1.5 | 2.6 ± 2.7 | 0.007** |
Frequency of Phototherapy (n/%) | 154/82 | 29/90 | 18/86 | 3/100 | 8/100 | 0.701 |
Frequency of blood exchange (n/%) | 28/15 | 4/12 | 3/14 | 0/0 | 1/13 | 0.934 |
Hospital stay (days) | 6.2 ± 4.1 | 5.6 ± 3.1 | 5.2 ± 3.1 | 4.6 ± 1.5 | 7.1 ± 3.5 | 0.254 |