Table 1 Diagnostic criteria for PFAPA

I. Regularly recurring fevers with an early age of onset (< 5 years of age)

II. Constitutional symptoms in the absence of upper respiratory infection with at least 1 of the following clinical signs:

a) aphtous stomatitis, b) cervical lymphadenitis, c) pharyngitis

III. Complete asymptomatic interval between episodes

IV. Normal growth and development