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Table 1 Clinical characteristics of the 13 patients with RMS and bone marrow metastasis

From: Clinical features and prognosis of paediatric rhabdomyosarcoma with bone marrow metastasis: a single Centre experiences in China

Case

Sex

age (year)

Primary site

Initial diagnosis

A

A

Size (cm)

Oberlin Score

Total

Bone

PAX/ FOXO

Pathol- ogical

Immunohistochemically

metastasis

metastasis

1

M

11.8

Groin

NHL

N

9

4

7

P

N

ERMS

Desmin(+),Vimentin(+),

MyoD1(+), Myogenin(+)

2

M

3.2

Chest wall

PPB

N

5

4

8

P

–

ERMS

Desmin(+), MyoD1(+), Myogenin(+)

3

F

2.9

chest wall

AL

Y

7.7

4

7

P

P

ARMS

Desmin(+),Myogenin(+), Vimentin(+),

4

M

2

Pelvic cavity

AML

Y

4

4

7

N

–

ARMS

Desmin(+), Myoglobin(+)

5

M

1.7

Lower jaw

AML

N

3.7

4

17

P

P

ARMS

Desmin(+),Vimentin (+), Myogenin(+)

6

M

5.8

cranial base

PPB

Y

6.6

4

4

P

N

ERMS

Desmin(+), MyoD1(+),Myogenin(+)

7

M

12

Nasopharynx

RMS

N

4.5

4

10

P

P

ARMS

Desmin(+), MyoD1(+), Myogenin(+)

8

M

8.4

Palm

NB

Y

3.1

4

9

P

P

ARMS

Desmin(+), MyoD2(+), Myogenin(+)

9

M

5.6

Bladder

RMS

N

7

4

4

P

N

ERMS

Desmin(+), MyoD1(+),Myogenin(+)

10

F

13

Mediastinum

PPB

Y

8.4

4

3

N

P

ARMS

Desmin(+), Vimentin(+), Myogenin(+)

11

F

14

Sole

RMS

N

2.4

4

4

P

P

ARMS

Desmin (+), Vimentin(+), MyoD1(+), Myogenin(+)

12

M

5.4

Pelvic cavity

HL

N

10

4

9

P

P

ARMS

Desmin(+), MyoD1(+), Myogenin(+)

13

M

2.1

Pelvic cavity

RMS

N

12.9

4

6

P

P

ARMS

Desmin(+), MyoD1(+),Myogenin(+)

  1. Abbreviations: M Male, F Female, NB Neuroblastoma, NHL Non-Hodgkin lymphoma, PPB Pleuropulmonary blastoma, AL Acute leukemia, AML acute myelocytic leukemia, HL Hodgkin's Lymphoma, AA Aplastic anemia, ARMS Alveolar rhabdomyosarcoma, ERMS Embryonal rhabdomyosarcoma, N NO, Y Yes, P PosItive, N Negative