From: Pediatric hemophagocytic lymphohistiocytosis: A rarely diagnosed entity in a developing country
Criteria at admission | Frequency %(n) | Median (IQR) |
---|---|---|
Fever ≥ 7 days | 71.4(15) | 17 days(6–30) |
Splenomegaly > 3 cm below rib limit | 61.9(13) | - |
Bicytopenia | 61.9(13) | - |
Hyperferritinemia > 500 mg/dl | 81.0(17) | 1866.5 ng/ml (889-10286) |
Hypertriglyceridemia (> 150 mg/dl) or hypofibrinogenemia (< 150 mg/dl) | 76.2(16) | 267 mg/dl (184–324) |
167.5 mg/dl (94–315) | ||
Hemophagocytosis in BM | 57.1(12) | - |
Decrease in NK cells or altered functionality | 14.3(3) | - |
No evidence of malignancy | 100.0(21) | - |
Genetic Testing for primary HLHa | 14.3(3) | - |