Table 1 Clinical findings reported among patients with CF in Ecuador
Clinical findings reported at CF Diagnosis | ||||
|---|---|---|---|---|
< 5 (%) | 6 to 10 (%) | 11 to 15 (%) | ≥ 16 (%) | |
Number of individuals (n) | 13 | 11 | 15 | 8 |
Familiar history with asymptomatic patient | 15.4 | 9.1 | 6.7 | 0.0 |
Symptoms | ||||
Persistent respiratory symptoms | 69.2 | 90.9 | 93.3 | 100.0 |
Persistent gastrointestinal symptoms | 38.5 | 0.0 | 6.7 | 0.0 |
Signs | ||||
Digital clubbing | 0.0 | 27.3 | 13.3 | 25.0 |
Abnormal liver function test | 7.7 | 0.0 | 0.0 | 0.0 |
Sinus disease | 0.0 | 9.1 | 6.7 | 25.0 |
Malnutrition | 23.1 | 18.2 | 33.3 | 25.0 |
Body mass index percentile (average) | a44.8 | a37.6 | a37.8 | a28.3 |
Score Shwachman – Kulczycki | ||||
Excellent | 53.9 | 63.6 | 33.3 | 25.0 |
Good | 46.1 | 27.3 | 20.0 | 12.5 |
Mild | 0.0 | 9.1 | 46.7 | 50.0 |
Moderate | 0.0 | 0.0 | 0.0 | 12.5 |
Severe | 0.0 | 0.0 | 0.0 | 0.0 |
Comorbidities | ||||
Cyrstic fibrosis related Diabetes | 0.0 | 0.0 | 6.7 | 37.5 |
Asthma | 0.0 | 36.4 | 40.0 | 25.0 |
Pulmonary Hypertension | 0.0 | 0.0 | 6.7 | 12.5 |
Celiac disease | 0.0 | 0.0 | 6.7 | 0.0 |
Cholelithiasis | 0.0 | 0.0 | 6.7 | 0.0 |
Allergic bronchopulmonary aspergillosis | 0.0 | 9.1 | 13.3 | 0.0 |
Pancreatitis | 0.0 | 18.2 | 0.0 | 0.0 |
Meconium ileus/other intestinal obstruction | 0.0 | 9.1 | 6.7 | 0.0 |