TY - JOUR AU - Piatti, G. AU - De Santi, M. M. AU - Farolfi, A. AU - Zuccotti, G. V. AU - D’Auria, E. AU - Patria, M. F. AU - Torretta, S. AU - Consonni, D. AU - Ambrosetti, U. PY - 2020 DA - 2020/04/13 TI - Exacerbations and Pseudomonas aeruginosa colonization are associated with altered lung structure and function in primary ciliary dyskinesia JO - BMC Pediatrics SP - 158 VL - 20 IS - 1 AB - Recurrent bacterial infections of the respiratory tract are one of the major clinical features of the primary ciliary dyskinesia (PCD), a rare genetic disease due to malfunctioning of motile cilia. Chronic infections and persistent inflammation of the respiratory system result in progressive lung disease. SN - 1471-2431 UR - https://doi.org/10.1186/s12887-020-02062-4 DO - 10.1186/s12887-020-02062-4 ID - Piatti2020 ER -