From: Congenital bronchopulmonary foregut malformation: systematic review of the literature
Clinical Features | Group | Total (n = 61) | ||||
---|---|---|---|---|---|---|
IA (n = 13) | IB (n = 4) | II (n = 18) | III (n = 23) | IV (n = 3) | ||
Sex | ||||||
 Male | 7 (53.8%) | 2 (50.0%) | 8 (44.4%) | 9 (39.1%) |  | 26 (42.6%) |
 Female | 6 (46.2%) | 2 (50.0%) | 10 (55.6%) | 9 (39.1%) | 3 (100%) | 30 (49.2%) |
 Not stated |  |  |  | 5 (21.7%) |  | 5 (8.2%) |
Age | ||||||
 Newborn | 13 (100%) | 3 (75.0%) | 10 (55.6%) | 12 (52.2%) |  | 38 (62.3%) |
 Infant (< 1 yr) |  |  | 5 (27.8%) | 2 (8.7%) | 1 (33.3%) | 8 (13.1%) |
 Child (< 18 yr) |  | 1 (25.0%) | 3 (16.7%) | 3 (13.0%) | 1 (33.3%) | 8 (13.1%) |
 Adult |  |  |  | 6 (26.1%) | 1 (33.3%) | 7 (11.5%) |
 Not Stated |  |  | 1 (5.6%) |  |  | 1 (1.6%) |
Side | ||||||
 Right | 9 (69.2%) | 4 (100%) | 14 (77.8%) | 14 (60.9%) | 3 (100%) | 44 (72.1%) |
 Left | 3 (23.1%) |  | 4 (22.2%) | 7 (30.4%) |  | 14 (23.0%) |
 Bilateral |  |  |  | 2 (8.7%) |  | 2 (3.3%) |
 Not stated | 1 (7.7%) |  |  |  |  | 1 (1.6%) |
Arterial supply | ||||||
 Systemic | 2 (15.4%) | 1 (25.0%) | 2 (11.1%) | 17 (73.9%) |  | 22 (36.1%) |
 Pulmonary | 3 (23.1%) |  | 11 (61.1%) | 2 (8.7%) | 1 (33.3%) | 17 (27.9%) |
 Not stated | 8 (61.5%) | 3 (75.0%) | 5 (27.8%) | 4 17.4%) | 2 (66.7%) | 22 (36.1%) |
Divagnostic method | ||||||
 UGI | 10 (76.9%) | 2 (50.0%) | 14 (77.8%) | 10 (43.5%) | 2 (66.7%) | 38 (62.3%) |
 CT | 2 (15.4%) | 1 (25.0%) | 4 (22.2%) |  |  | 7 (11.5%) |
 Bronchoscopy | 1 (7.7%) |  |  |  |  | 1 (1.6%) |
 Intraoperative |  | 1 (25.0%) |  | 7 (30.4%) |  | 8 (13.1%) |
 Other |  |  |  | 6 (26.1%) | 1 (33.3%) | 7 (11.5%) |
Outcome | ||||||
 Survive | 7 (53.8%) | 2 (50.0%) | 12 (66.7%) | 14 (60.9%) | 3 (100%) | 38 (62.3%) |
 Death | 4 (30.8%) | 2 (50.0%) | 1 (5.6%) | 1 (4.3%) | 0 (0) | 8 (13.1%) |
 Not stated | 2 (15.4%) |  | 5 (27.8%) | 8 (34.8%) |  | 15 (24.6%) |