From: Clinical manifestations and anti-TNF alpha therapy of juvenile Behçet’s disease in Taiwan
Characteristic | ||
---|---|---|
Male gender, n (%) | 22 | (40.0) |
Age at disease onset (years) | 11 | (0.1–16.0) |
Age at diagnosis (years) | 13 | (0.1–16.0) |
Time to diagnosis (years) | 0 | (0.0–8.0) |
Diagnosis criteria, n (%) | ||
ICBD | 50 | (90.9) |
PEDBD | 20 | (36.4) |
No criteria met | 5 | (9.1) |
Clinical presentations, n (%) | ||
Recurrent oral aphthous ulcers | 55 | (100) |
Genital ulceration | 38 | (69.1) |
Skin involvement | 20 | (36.4) |
Ocular involvement | 15 | (27.3) |
Neurologic signs | 2 | (3.6) |
Vascular signs | 1 | (1.8) |
Gastrointestinal symptoms | 16 | (29.1) |
Arthritis/arthralgia | 15 | (27.3) |