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Table 1 Characteristics of the patients with juvenile Behçet’s disease (n = 55)

From: Clinical manifestations and anti-TNF alpha therapy of juvenile Behçet’s disease in Taiwan

Characteristic

Male gender, n (%)

22

(40.0)

Age at disease onset (years)

11

(0.1–16.0)

Age at diagnosis (years)

13

(0.1–16.0)

Time to diagnosis (years)

0

(0.0–8.0)

Diagnosis criteria, n (%)

 ICBD

50

(90.9)

 PEDBD

20

(36.4)

 No criteria met

5

(9.1)

Clinical presentations, n (%)

 Recurrent oral aphthous ulcers

55

(100)

 Genital ulceration

38

(69.1)

 Skin involvement

20

(36.4)

 Ocular involvement

15

(27.3)

 Neurologic signs

2

(3.6)

 Vascular signs

1

(1.8)

 Gastrointestinal symptoms

16

(29.1)

 Arthritis/arthralgia

15

(27.3)

  1. For quantitative and ordinal data median and range are presented
  2. ICBD International Criteria for Behçet’s Disease, PEDBD Pediatric Behçet’s Disease