Table 1 Pediatric classic Kaposi’s sarcoma in literature review

Origin

Mediterranean Basin

Other countries

Mediterranean Basin

Other countries

22

10

2

2

36

Age

 0- < 10

11

7

1

2

21

 10- < =15

8

3

1

0

12

 NA

3

0

0

3

Sex

 Male

15

8

2

2

27

 Female

6

1

0

0

7

 NA

1

1

0

0

2

Clinical findings

 Lymph node (s)

 Yes

10

1

0

2

13

 No

2

5

0

0

7

 NA

10

4

2

0

16

 Visceral involvement

 Yes

8

3

1

2

14

 No

6

4

1

0

11

 NA

8

3

0

0

11

Diagnosis

 Skin biopsy

18

8

0

0

26

 Lymph node biopsy

1 ^a

0

1

2

3

 NA

4

2

1

0

7

 HHV-8 status

 Positive

12

2

0

0

14

 Negative

1 ^b

0

0

0

1

 Non-conclusive

1

0

0

0

1

 Test not yet available (old reports)

8

8

2

2

20

Immunity status

 Identified Immunodeficiency

5

0

0

0

5

 1- IFN-gamma-R1 deficiency

2

0

0

0

 2- Wiskott-Aldrich syndrome

2

0

0

0

 3- Inherited human OX40 deficiency

1

0

0

0

 Unidentified Immunodeficiency

2

2

0

0

4

 NA

15

8

2

2

27

Treatment

 Given treatment

21

 No treatment

1

1

0

0

2

 NA

6

5

2

0

13

Outcome

 Survived

10

5

0

1

16

 Dead

6

1

1

1

9

 NA

6

4

1

0

11