From: The etiologies of non-CF bronchiectasis in childhood: a systematic review of 989 subjects
Total number | % of total | |
---|---|---|
B cell disorders | 97 | 74% |
IgG deficiency* | 63 | 48% |
IgG subclass deficiency | 24 | 18% |
IgA deficiency | 9 | 7% |
B cell deficiency NOS | 1 | 1% |
T cell disorders | 9 | 7% |
Hyper IgE syndrome | 3 | 2% |
Hyper IgM syndrome | 2 | 2% |
T Cell deficiency | 3 | 2% |
Chronic mucocutaneous candidiasis | 1 | 1% |
Combined immunodeficiency | 13 | 10% |
Severe combined immunodeficiency** | 9 | 7% |
Ataxia-telangiectasia | 2 | 2% |
Wiskott-Aldrich syndrome | 2 | 2% |
Chronic granulomatous disease | 7 | 5% |
Barre lymphocyte syndrome/MHC class II deficiency | 2 | 2% |
Mannose-binding protein deficiency | 1 | 1% |
Other disorders | 2 | 2% |