Table 1 ICD codes used in the search for cases of progressive encephalopathy in children born between 1985 and 2003
From: Incidence rates of progressive childhood encephalopathy in Oslo, Norway: a population based study
Diseases | ICD-10 (>1998) | ICD-9 (1986–1998) | ICD-8 (<1986) |
|---|---|---|---|
Inborn errors of metabolism | |||
Amino acidopathies | E70–E72 | 270 | 270 |
Carbohydrate metabolism | E74 | 271 | 271 |
Sphingolipids and other lipid storage disorders | E75 | 272 | 272 |
Glucoseaminoglycans (mucopolysaccharidoses) | E76 | 277.5 | 273 |
Glycoprotein metabolism | E77 | 277.5–277.9 | 270–273 |
Purin and pyrimidine | E79 | 277.2 | 270 |
Mineral metabolism | E83 | 275 | 273 |
Other aetiological diagnoses | |||
Systemic atrophies primarily affecting CNS | G10–G13 | 333 | 331 |
Extrapyramidal and other movement disorders | G20–G26 | 333 | 332 |
Other CNS degenerative diseases | G30–G32 | 340 | 340–341 |
Demyelinating disorders | G35–G37 | 340–341 | 340–341 |
HIV with dementia | B22 | - | - |
Unspecified/Descriptive diagnoses | |||
Unspecified metabolic disease | E88.9 | NA | NA |
Encephalopathy | G93.4; G93.9 | 348.3; 348.9 | 781.7 |
Other CNS disease | G96 | 348.3 | NA |