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Table 1 Respiratory chain analysis of patient's skeletal muscle tissue

From: Neonatal presentation of ventricular tachycardia and a Reye-like syndrome episode associated with disturbed mitochondrial energy metabolism

Enzyme Complex Activity
(μmol/min-1/g-1)
Normal reference mean ± 1 SD
Cytochrome c oxidase IV 2.56* (2.8 ± 0.52)
Succinate cytochrome c reductase II + III 0.55 (0.7 ± 0.23)
NADH cytochrome c reductase I + III 1.44 (1.02 ± 0.38)
NADH dehydrogenase I 29.32 (35.48 ± 7.07)
Citrate synthase   15.01 (9.88 ± 2.55)
Succinate dehydrogenase II 1.15 (1 ± 0.53)
  1. NADH = reduced nicotinamide adenine dinucleotide * Data represent the mean of 2 independent analyses on different muscle homogenates
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