CCC categories | KID* (Weighted N = 7,337,017) | NEDS (Weighted N = 29,741,986) | ||||
---|---|---|---|---|---|---|
 | CCC v1 | CCC v2 | % Change | CCC v1 | CCC v2 | % change |
Neurologic and neuromuscular | 1.36 (1.35–1.37) | 2.28 (2.26–2.30) | 67.64% | 0.31 (0.26–0.37) | 0.52 (0.43–0.61) | 67.74% |
Cardiovascular | 3.29 (2.27–3.30) | 2.32 (2.30–2.33) | –29.48% | 0.43 (0.38–0.48) | 0.48 (0.42–0.54) | 11.63% |
Respiratory | 0.92 (0.91–0.93) | 0.97 (0.96–0.98) | 5.43% | 0.08 (0.07–0.11) | 0.13 (0.10–0.16) | 62.50% |
Renal and urologic | 0.75 (0.74–0.76) | 1.21 (1.12–1.22) | 61.33% | 0.08 (0.07–0.10) | 0.13 (0.11–0.15) | 62.50% |
Gastrointestinal | 0.62 (0.61–0.63) | 2.02 (2.00–2.03) | 225.81% | 0.09 (0.08–0.10) | 0.39 (0.30–0.48) | 333.33% |
Hematologic or immunologic | 1.32 (1.30–1.33) | 1.60 (1.58–1.61) | 21.21% | 0.34 (0.28–0.39) | 0.41 (0.35–0.47) | 20.59% |
Metabolic | 0.84 (0.83–0.85) | 1.11 (1.10–1.12) | 32.14 | 0.14 (0.12–0.16) | 0.19 (0.16–0.21) | 35.71% |
Other congenital or genetic defect | 1.64 (1.63–1.65) | 1.64 (1.63–1.65) | 0.00% | 0.31 (0.27–0.36) | 0.31 (0.27–0.36) | 0.00% |
Malignancy | 2.10 (2.08–2.11) | 1.64 (1.63–1.65) | –21.91% | 0.21 (0.17–0.25) | 0.16 (0.12–0.20) | -23.81% |
Neonatal | --- | 1.14 (1.13–1.15) | --- | --- | 0.03 (0.02–0.04) | --- |
Technology dependency | --- | 2.64 (2.62–2.65) | --- | --- | 0.46 (0.35–0.58) | --- |
Transplantation | --- | 0.38 (0.37–0.38) | --- | --- | 0.05 (0.04–0.07) | --- |
CCC (Any CCC) | 10.56 (10.53–10.59) | 11.57 (11.53–11.59) | 9.56% | 1.83 (1.60–2.06) | 2.27 (1.97–2.72) | 24.04% |