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Table 1 Laboratory data on admission

From: 10-year-old girl with life-threatening idiopathic systemic capillary leak syndrome: a case report

WBC

41 × 103/μL

(3.9-6.60 × 103/μL)

C1-INH

150%

(70–130%)

RBC

7.99 × 106/μL

(4.08-4.81 × 106/μL)

C3

23.6 IU/L

(65.0-141.0 IU/L)

Hb

23.3 g/dl

(12.0-14.7 g/dl)

C4

6.1 IU/L

(13.0-40.0 IU/L)

Ht

64.4%

(37.0-44.6%)

CH50

15.1 IU/L

(31–48 IU/L)

PLT

25.7 × 104/μL

(18.0-36.5 × 104/μL)

ANA

<40

(<40)

   

VEGF

<20 pg/ml

(<20 pg/ml)

   

IL-6

85.8 pg/ml

(<420 pg/ml)

Alb

2.3 g/dL

(3.5-5.0 g/dL)

G-CSF

217 pg/ml

(<39 pg/ml)

BUN

42 mg/dL

(8–20 mg/dL)

   

CRE

2.1 mg/dL

(0.42-0.68 mg/dL)

Urinalysis

  

Na

130 mEq/L

(135–145 mEq/L)

protein

100 mg/dL

 

K

4.8 mEq/L

(3.3-5.0 mEq/L)

blood

3+

 

Cl

98 mEq/L

(96–109 mEq/L)

RBC

>100 /HPF

 

Ca

7.6 mg/dL

(8.5-10.5 mg/dL)

Bence-Jones Protein

(−)

 

CPK

399 U/L

(12–170 U/L)

   

CRP

3.24 mg/dL

(0–0.30 mg/dL)

Culture (Blood, Urine, Stool): (−)

  
  1. C1-INH: C1-esterase inhibitor, ANA: antinuclear antibody, VEGF: vascular endothelial growth factor IL-6, G-CSF: granulocyte colony-stimulating factor.